Very long-chain specific acyl-CoA dehydrogenase, mitochondrial

Summary
UniProt ID
P50544
Gene Symbol
  • Acadvl
  • Vlcad
Gene ID
11370
Organism
Mus musculus (house mouse)
GlyGen
P50544
PubChem
P50544
RaftProt
P50544
Re-Glyco
P50544
Annotation
Keyword
  • 3D-structure
  • Acetylation
  • FAD
  • Fatty acid metabolism
  • Mitochondrion inner membrane
  • Oxidoreductase
  • Phosphoprotein
  • Reference proteome
  • S-nitrosylation
  • Transit peptide
Gene Ontology (GO)
Sequence
MQSARMTPSVGRQLLRLGARSSRSTTVLQGQPRPISAQRLYAREATQAVLDKPETLSSDASTREKPARAESKSFAVGMFKGQLTIDQVFPYPSVLSEEQAQFLKELVGPVARFFEEVNDPAKNDALEKVEDDTLQGLKELGAFGLQVPSELGGLGLSNTQYARLAEIVGMHDLGVSVTLGAHQSIGFKGILLYGTKAQREKYLPRVASGQALAAFCLTEPSSGSDVASIRSSAIPSPCGKYYTLNGSKIWISNGGLADIFTVFAKTPIKDAATGAVKEKITAFVVERSFGGVTHGLPEKKMGIKASNTSEVYFDGVKVPSENVLGEVGDGFKVAVNILNNGRFGMAATLAGTMKSLIAKAVDHATNRTQFGDKIHNFGVIQEKLARMAILQYVTESMAYMLSANMDQGFKDFQIEAAISKIFCSEAAWKVADECIQIMGGMGFMKEPGVERVLRDIRIFRIFEGANDILRLFVALQGCMDKGKELTGLGNALKNPFGNVGLLMGEAGKQLRRRTGIGSGLSLSGIVHPELSRSGELAVQALDQFATVVEAKLVKHKKGIVNEQFLLQRLADGAIDLYAMVVVLSRASRSLSEGYPTAQHEKMLCDSWCIEAATRIRENMASLQSSPQHQELFRNFRSISKAMVENGGLVTGNPLGI
Glycosylation Sites
Displaying 1 entry
Position Description PubMed ID GlyTouCan ID Source
366
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying 1 entry
Pathway Name Organism
Beta oxidation of palmitoyl-CoA to myristoyl-CoA Mus musculus
Disease
Displaying 1 entry
DO ID Disease Name Source
DOID:0080155 very long chain acyl-CoA dehydrogenase deficiency

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International Collaboration

GlyCosmos is a member of the GlySpace Alliance together with GlyGen and Glycomics@ExPASy.

Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 7, 2025