Alpha-L-iduronidase

Summary
UniProt ID
Q9VKJ8
Gene Symbol
  • CG6201
  • Idua
Gene ID
34544
Organism
Drosophila melanogaster (fruit fly)
PubChem
Q9VKJ8
Re-Glyco
Q9VKJ8
Annotation
Keyword
  • Disulfide bond
  • Glycoprotein
  • Glycosidase
  • Lysosome
  • Reference proteome
  • Signal
Gene Ontology (GO)
Displaying 1 entry
GO Term
lysosome
Subcellular Location(GO Annotation)

Subcellular in which this glycoprotein is expressed are highlighted in blue.

Displaying 1 entry
GO Term
L-iduronidase activity
Sequence
MLSLLLVLTTLARIHAHYTSGDVVYHTMPHFWTGVGFCPAGRIDHEGISAALGDPALRLNLRLIAALPVGAVTHIRIHWLLELIQFWQYDPSGIPIYDFSKFDDFIDFLHEELRLSPVLEWMGNLGGVFSENPMQQSFYWEHLVKTTINHQIARHGSSRLVNWRYETWNEPDLRGYNKQNFTAHTFLDYVQAVRRGLSKAGNLDNQDGKVPLPMYRSLRGPAGLFKDSNHPLCWNLLELCSQRVVYCPIDILTFHRKGIEGTATEIVNGSLSLMAKIYEEYPNLKQLPVANDEADPVAGWSTSRDFQADVRYGITLISTVMQFWHAKLAGGPLSRLESISHDNAFLSYHPHEFTQRTLLAHFRMNETKPPHSQLVQKPVYAALGMLAKLGTRAADVEMVNMDTKHSVQVLRTVSGGLGGPGQYMATIFLSPEEAGPKMTAFHHKYTLNMSIANESAFVTELLVPKETDPYYIWQQAGSPAYPNATLREAMRRAQAPRLYKTGPIWQYNSELVINSASIPLPWAMLLRVCSASWPKLRRPQQLSIAEVTQREVFISWMEHPKSTQCLLSYEVWFKERDNLGRSADWMLISQGWHLPYPSFQYAPGDKGSVNGFYKVRGVDVFNETSPYSQIVEYLEL
Glycosylation Sites
Displaying all 7 entries
Position Description PubMed ID GlyTouCan ID Source
180 N-linked (GlcNAc...) asparagine
268 N-linked (GlcNAc...) asparagine
365 N-linked (GlcNAc...) asparagine
448 N-linked (GlcNAc...) asparagine
453 N-linked (GlcNAc...) asparagine
483 N-linked (GlcNAc...) asparagine
622 N-linked (GlcNAc...) asparagine
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying all 2 entries
Pathway Name Organism
CS/DS degradation Drosophila melanogaster
HS-GAG degradation Drosophila melanogaster
Disease
Displaying 1 entry
DO ID Disease Name Source
DOID:12802 mucopolysaccharidosis I

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International Collaboration

GlyCosmos is a member of the GlySpace Alliance together with GlyGen and Glycomics@ExPASy.

Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 7, 2025